A retroperitoneal myopericytoma: The first case located at the retroperitoneal area and not originate from the kidneys

A 25-year-old woman had a mass of approximately 65 cm × 33 cm × 102 cm, located in the left paraaortic area on CT scan. It was diagnosed as retroperitoneal malignant neoplasm on imaging. Afterward, open retroperitoneal tumor excision was performed. At laparotomy, the mass was carefully dissected from the ureter, renal artery, and aorta and excised as en-bloc. The pathological result was “myopericytoma.” Histologically, the pathological findings characterized a pericytic neoplasm characterized by a perivascular growth of myoid tumor cells. In addition, there were uniform, oval-shaped cells with eosinophilic cytoplasm arranged in short fascicles around blood vessels. The cytologic atypia and mitoses were absent. There are many different tumors in the retroperitoneal area. Most of these lesions are malign nature. Nevertheless, for each benign and malign neoplasm, the preoperative imaging method is generally similar. This present case showed the significant findings of myopericytoma, a benign pathology located in the retroperitoneal area.

Surgical Treatment of Primary Pulmonary Myopericytoma

Myopericytoma is a benign tumor that occurs in soft tissues. Myopericytoma in the lungs is very rare. We report the case of a 63-year-old woman presenting with cavitary masses in the left lung and multiple tiny nodules in both lungs. She underwent surgery, and a histological examination revealed primary pulmonary myopericytoma.

Myopericytoma - A Unifying Term Or A Unique Entity?

Myopericytoma are uncommon, slow-growing benign perivascular neoplasms that show hemangiopericytoma-like vascular pattern. We report a 52-year-male patient with a painless palpable nodule in the left thumb for the past 9 months. The mass, on the thenar aspect, was 15x12mm in size. X-ray revealed a soft tissue swelling with no bony association. The excised nodule was a non-capsulated, well-circumscribed vascular neoplasm composed of proliferating spindle to ovoid bland cells with eosinophilic cytoplasm. A concentric perivascular arrangement of the cells was seen interspersed by thin-walled, branching, staghorn blood vessels. Nuclear atypia, mitotic figures and necrosis were not observed. Immunohistochemistry revealed diffuse positivity of the tumour cells for smooth muscle actin while staining negative for CD34 and desmin - features suggestive of origin from the perivascular myoid cell. Morphological features of myopericytoma are shared with hemangiopericytoma, glomus tumors, myofibroma and solitary fibrous tumour which form the important differential diagnoses. It is a relatively newly described disease entity recognized by the World Health Organisation classification of tumours.

Myopericytoma of lip: A rare lesion in an unusual location.

Myopericytoma is a rare benign tumor with perivascular myoid differentiation. It shares histomorpholoic features with the so-called hemangiopericytoma, myofi broma and glomus tumor. We hereby report the case of a 14-year-old boy who presented with a slowly growing, painless, fi rm mass on upper lip, diagnosed as myopericytoma on the basis of histopathology and immunohistochemistry. To the best of our knowledge, this is only the second such reported case.

A Case of Myopericytoma on the Lower Leg

Myopericytoma (MP) is a benign tumor composed of cells that show apparent differentiation towards putative perivascular myoid cells called myopericytes. It arises most commonly in the dermis or subcutaneous tissue of the extremities in adults. The most common presentation is a well-circumscribed, slow-growing painless firm mass. A 45-year-old woman presented with a 2-year history of a painless, slowly growing 0.9x0.7 cm sized firm mass in the subcutaneous tissue of the posterior side of the right lower leg. We presumed this lesion to be an epidermal cyst, pilomatricoma or calcinosis cutis and performed an excisional biopsy. The histologic examination showed that it was composed of spindle-shaped myoid-appearing cells in a concentric arrangement, intimately associated with thin-walled vascular channels. Lesional spindle cells were diffusely positive for smooth muscle actin and were negative for CD34, desmin and S100 protein. From these findings, we diagnosed this lesion as a myopericytoma.

Myopericytoma Involving the Parotid Gland as Depicted on Multidetector CT

Myopericytoma is a newly proposed subgroup of perivascular tumors in the World Health Organization classification of soft tissue tumors. In this study, we report a case of a benign myopericytoma with detailed multidetector CT (MDCT) findings in the parotid gland, a location that has not been described for this type of tumor previously. The clinical presentation, imaging features, histopathological and immunohistochemical findings, and the differential diagnosis with other tumors in the parotid gland are described and reviewed.

Myopericytoma-type Perivascular Myoma Arising on the Auricle of the Ear / 대한피부과학회지

The concept of perivascular myomas was recently proposed to designate perivascular myoid tumors arising from pleuripotent perivascular cells like smooth muscle cell cells, pericytes and glomus cell. They represent a histological continuum between three categories; myofibromatosis, glomangiopericytoma and myopericytoma. Myopericytoma is a rare, soft tissue tumor that primarily occurs in the skin and the subcutaneous and soft tissues of the extremities, but very few cases have been reported in other locations, which occurred in our present case. We herein report on a rare case of myopericytoma that developed on an unusual location, that is, the ear. The patient was a 35-year-old man who had a painless, slowly-growing red nodule on the upper auricle of the right ear for 5 years. The nodule was revealed to be a well-circumscribed mass composed of round to oval cells that strongly expressed smooth muscle actin. These cells were arranged in the concentrically multilayered pattern and they were surrounded by small to medium-sized vessels.

A Case of Myopericytoma in the Neck / 대한이비인후과학회지

A myopericytoma is a rare mesenchymal neoplasm composed of oval to spindle-shaped myoid appearing cells with a striking tendency for concentric perivascular growth. The vast majority of lesion is in the dermis and subcutaneous tissue of extremities. Very few cases have been reported in other locations. We hereby present, with a literature review, a case of myopericytoma in the neck.